Multicystic dysplasia of the upper segment of the double kidney with ipsilateral ureterocele and vesicoureteral reflux in an infant: a case report

Abstract

Multicystic kidney dysplasia is a common nonhereditary developmental anomaly. However, multicystic dysplasia with doubling of the urinary tract is a rather rare pathology, which is often accompanied by the presence of ureterocele and high vesicoureteral reflux. Few clinical cases have been described in the current literature and there is no unambiguous tactic for the management of such patients.

Purpose - to present a rare case of combined urinary tract anomaly to draw the attention of paediatric urologists to possible anomalies of the urinary system.

Clinical case. A case of surgical treatment of an infant with the above pathology is described. The child was initially qualified for surgery for recurrent urinary tract infection and a functional upper segment of the left kidney with complete duplication. A ureterocele dissection on the ipsilateral side was performed beforehand.

Given that multicystic dysplasia in urinary tract doubling with ureterocele and reflux is a rare pathology, it was diagnosed intraoperatively. Laparoscopic removal of the cystic mass and ureterocele was performed. The postoperative period was uneventful.

Conclusions. Multicystic dysplasia with ureterocele and reflux is a rare pathology. It is always necessary to pay attention to the peculiarities of diagnostics in case of suspected combined anomaly of the urinary tract.

The study was conducted in accordance with the principles of the Declaration of Helsinki. The study protocol was approved by the Local Ethics Committee of the institution mentioned in the work. The informed consent of the child’s parents was obtained for the study.

No conflict of interests was declared by the authors.