Clinical case of congenital vagina and cervical malformations in adolescent girl
DOI:
https://doi.org/10.15574/PS.2024.4(85).123129Keywords:
congenital vaginal atresia, congenital cervical atresia, treatment, hysterectomyAbstract
Congenital malformations of the female genital organs consist of a group of various deviations from normal anatomical structure. Management of the congenital abnormalities of the female genital tract depends on the type of malformation and includes both endoscopic and conventional surgeries.
The aim of this study was to present the case of congenital vaginal atresia associated with cervical atresia in adolescent female patient, in which hysterectomy was performed.
Clinical case. During surgery, due to the acute appendicitis in a female patient with mental retardation, the uterine congenital malformation was suspected. After further investigation, the diagnosis of vaginal and cervical aplasia was established. She received conservative therapy (peroral contraceptives), but there were disturbances in the medication regime that caused the necessity of rehospitalization and emergent surgery – hysterectomy with the right-side tubectomy and left-side adnexectomy. The postoperative course was uncomplicated.
Conclusion. Girls of prepubertal and pubertal age with primary amenorrhea and cyclic abdominal pain should always consulted by a gynecologist in order to confirm/exclude malformations of uterus and genital tracts, their timely treatment, and prevention of possible complications. The choice of surgical treatment for vaginal atresia combined with cervical atresia should be individual in each case, bearing in mind associated pathology and social status of the child.
The research was carried out in accordance with the principles of the Declaration of Helsinki. The research protocol was approved by the Local Ethics Committee of the institution mentioned in the work. The informed consent of the patients was obtained for the research.
No conflict of interests was declared by the authors.
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