Treatment of membranous atresia of the stomach, combined with epidermolysis bullosa, in newborns. a literature overview and own observations
DOI:
https://doi.org/10.15574/PS.2017.55.92Keywords:
gastric atresia, pyloric web, epidermolysis bullosa, newbornsAbstract
The article presents literature data on prevalence, clinical picture, diagnosis, treatment and prognosis of associated birth defects – membranous pyloric atresia and epidermolysis bullosa in newborns. Two own observations of these severe defects are also given. The authors concluded that the presence of epidermolysis bullosa in a neonate requires a follow-up examination concerning possible pyloric atresia. The prognosis for the combined stomach atresia and epidermolysis bullosa largely depends upon the severity of the digestive tract and upper respiratory tract lesions, as well as septic complications.References
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