Rare defect of development – congenital segmental dilation of the colon in the newborn. literature review and own observation

Authors

  • O. D. Fofanov Ivano-Frankivsk National Medical University, Ukraine, Ukraine https://orcid.org/0000-0003-1437-4161
  • V. O. Fofanov Ivano-Frankivsk National Medical University, Ukraine, Ukraine
  • O. Yu. Fofanova Ivano-Frankivsk National Medical University, Ukraine, Ukraine
  • Ya. Ya. Sicoryn Ivano-Frankivsk National Medical University, Ukraine, Ukraine

DOI:

https://doi.org/10.15574/PS.2019.63.109

Keywords:

congenital segmental dilation of the colon, newborn babies

Abstract

The article presents literary data on distribution, morphological signs, clinic, diagnostics and treatment of rare defect of the digestive tract – congenital segmental dilation of the colon (CSDC) in children. The actual clinical observation of this defect in a newborn child is also presented. In newborns the defect is diagnosed very rarely and is manifested by symptoms of intestinal obstruction, mostly is diagnosed intraoperatively. In older children the clinical manifestation resembles Hirschsprung’s disease. The authors came to the conclusion that CSDC in newborn babies can be diagnosed before surgery. Its patognomonic features are the presence of large cystic expansion of the large intestine according to clinical and ultrasonographic data, absence of the motility of the affected (extended) department with preservation of the motility of proximal and distal regions of the colon according to irrigography data. In the pathomorphological study, according to the literature, in the affected area of the colon, as in the distal part, normal ganglion cells are found. However, in our observation, ganglia with signs of dysplasia in the enlarged and distal areas of the colon were detected. The tactics of surgical correction largely depend on the localization and length of СSDC and is different from operations in the Hirschsprung’s disease. Therefore, it is important to carefully differentiate these defects.

References

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Issue

No. 2(63) (2019): Paediatric surgery. Ukraine

Section

Clinical case

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