Rare anorectal malformation – a congenital pouch colon in neonates: literature review and own observation

Authors

  • O. D. Fofanov Ivano-Frankivsk National Medical University, Ukraine, Ukraine https://orcid.org/0000-0003-1437-4161
  • V. O. Fofanov Ivano-Frankivsk National Medical University, Ukraine, Ukraine
  • V. V. Banasevych CI Ivano-Frankivsk Oblast Children's Clinical Hospital, Ukraine, Ukraine

DOI:

https://doi.org/10.15574/PS.2018.59.72

Keywords:

congenital pouch colon, anorectal malformations, newborns

Abstract

The article presents literary data on distribution, morphological signs, clinics, diagnostics and treatment of rare defects (especially in the European countries) – congenital pouch colon (CPC) in association with anorectal agenesis in newborns. The actual clinical observation of this combined defect in a newborn girl is also given. The authors concluded that the pathognomonic feature of CPC is the presence of a large gas bubble of the colon, which occupies more than 50% of the abdominal width in a child with anorectal agenesis on the plain abdominal X-ray or invertogram, and ultrasound signs of cystic enlargement of the colon. Tactics of surgical correction and prognosis are largely dependent upon the type of CPC and of associated anorectal malformation.

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Issue

No. 2(59) (2018): Paediatric Surgery. Ukraine

Section

Clinical case

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